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KMID : 0816120130160020127
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Korean Journal of Pediatric Gastroenterolology and Nutrition
2013 Volume.16 No. 2 p.127 ~ p.130
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A Case of Rapunzel Syndrome
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Kim Joon-Sung
Nam Chang-Woo
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Abstract
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Rapunzel syndrome refers to a very rare condition in which swallowed hair forms a gastric trichobezoar that has a long tail extending into the small bowel. We describe a case of Rapunzel syndrome in an 8-year-old girl who presented with abdominal mass, epigastric pain and vomiting. Abdominal computed tomography scan showed a markedly dilated stomach filled with coarse heterogeneous materials. Upper gastrointestinal endoscopy revealed a huge hairy ball with a tail extending through the pylorus. We performed a surgical laparotomy and successfully removed a huge trichobezoar with a long tail extending into the middle portion of jejunum. Psychiatric consultation with review showed her past history of trichotillomania and trichophagia 4 years ago. But her parents denied further psychiatric therapy and she was lost to the follow-up. Rapunzel syndrome should be included in the differential diagnosis in children with chronic abdominal pain and trichophagia.
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KEYWORD
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Rapunzel syndrome, Bezoars, Trichotillomania, Trichophagia, Abdominal pain
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